{"id":5871,"date":"2020-03-04T22:33:27","date_gmt":"2020-03-04T19:33:27","guid":{"rendered":"https:\/\/www.bursacocukkardiyoloji.com\/?p=5871"},"modified":"2021-12-23T11:41:41","modified_gmt":"2021-12-23T08:41:41","slug":"fetal-eko-2","status":"publish","type":"post","link":"https:\/\/www.bursacocukkardiyoloji.com\/index.php\/2020\/03\/04\/fetal-eko-2\/","title":{"rendered":"Fetal EKO"},"content":{"rendered":"\n<p>Gebelikte bebe\u011fin kalp anomalileri a\u00e7\u0131s\u0131ndan de\u011ferlendirilmesini sa\u011flayan <strong>ultrasonografik<\/strong> bir g\u00f6r\u00fcnt\u00fcleme y\u00f6ntemi. Do\u011fumsal kalp hastal\u0131klar\u0131, s\u0131k g\u00f6r\u00fclmesine ra\u011fmen, rutin ultrasonografik inceleme esnas\u0131nda en s\u0131k g\u00f6zden ka\u00e7\u0131r\u0131lan anomalidir.<\/p>\n\n\n\n<p>Do\u011fumda en s\u0131k rastlan\u0131lan anomali olan Do\u011fumsal Kalp Hastal\u0131klar\u0131, canl\u0131 yenido\u011fanlar\u0131n 1\/100\u2019 inde g\u00f6r\u00fclmekte olup kromozom anormalisi varl\u0131\u011f\u0131nda s\u0131kl\u0131\u011f\u0131 6-7 kat daha artmaktad\u0131r. Do\u011fumsal kalp hastal\u0131klar\u0131, \u00f6nemli bir sa\u011fl\u0131k sorunu ve en s\u0131k rastlan\u0131lan bir anomali olmas\u0131na ra\u011fmen,&nbsp;<strong>rutin ultrasonografik<\/strong>&nbsp;inceleme esnas\u0131nda en s\u0131k g\u00f6zden ka\u00e7\u0131r\u0131lan anomalidir.<\/p>\n\n\n\n<p><strong>Fetal kalp muayenesi<\/strong>&nbsp;3 de\u011fi\u015fik y\u00f6ntemle yap\u0131labilmektedir.&nbsp;<strong>Temel taramada<\/strong>&nbsp;kalbin 4-odac\u0131kl\u0131 yap\u0131s\u0131,&nbsp;<strong>Detayl\u0131 temel taramada<\/strong>&nbsp;kalbin 4-odac\u0131k yap\u0131s\u0131 ve b\u00fcy\u00fck damar \u00e7\u0131k\u0131\u015flar\u0131n\u0131n birlikte de\u011ferlendirilmesi ile yap\u0131lmaktad\u0131r. Temel tarama ve detayl\u0131 temel tarama, t\u00fcm gebelere uygulanmaktad\u0131r. T\u00fcm gebelere yap\u0131lmayan&nbsp;<strong>Fetal ekokardiyografide<\/strong>&nbsp;ise kardiak yap\u0131n\u0131n ve fonksiyonun detayl\u0131 analizi yap\u0131lmaktad\u0131r. Fetal ekokardiyografi,&nbsp;<strong>do\u011fumsal kalp hastal\u0131\u011f\u0131 riskinin y\u00fcksek oldu\u011fu&nbsp;<\/strong>veya&nbsp;<strong>temel tarama<\/strong>&nbsp;ya da&nbsp;<strong>detayl\u0131 temel taramada<\/strong>&nbsp;<strong>bir kalp anomalisinden \u015f\u00fcphe edildi\u011fi<\/strong>&nbsp;durumlarda uygulanmaktad\u0131r.<\/p>\n\n\n\n<p><strong>Do\u011fumsal Kalp Hastal\u0131\u011f\u0131 i\u00e7in artm\u0131\u015f riske sahip olanlar:<\/strong><\/p>\n\n\n\n<ol class=\"wp-block-list\"><li>Annede&nbsp;<strong>\u015feker hastal\u0131\u011f\u0131<\/strong>&nbsp;varl\u0131\u011f\u0131: 5 kat daha s\u0131k<\/li><li>Annede kontrols\u00fcz&nbsp;<strong>fenilketon\u00fcri<\/strong>&nbsp;hastal\u0131\u011f\u0131 varl\u0131\u011f\u0131: 10-15 kat daha s\u0131k<\/li><li>Annede&nbsp;<strong>Anti-Ro\/SSA<\/strong>&nbsp;veya&nbsp;<strong>anti-La\/SSB antikor<\/strong>&nbsp;varl\u0131\u011f\u0131: tam AV Blok, %1-5<\/li><li><strong>Rubella<\/strong>&nbsp;(K\u0131zam\u0131k\u00e7\u0131k) enfeksiyonu ge\u00e7irme: a\u015f\u0131lama nedeniyle nadir<\/li><li><strong>IVF<\/strong>&nbsp;gebelik: r\u00f6latif risk %1-3<\/li><li>Annenin&nbsp;<strong>epilepsi ilac\u0131<\/strong>&nbsp;(karbamazepin, valproat, fenitoin, hydantoin) kullanmas\u0131: zay\u0131f risk<\/li><li><strong>Anne, baba&nbsp;<\/strong>ve<strong>&nbsp;karde\u015flerinde&nbsp;<\/strong>do\u011fumsal kalp hastal\u0131\u011f\u0131 bulunmas\u0131: mutlak risk %3-7, ikinci derece akrabalarda varl\u0131\u011f\u0131nda &lt;%2<\/li><li>Kad\u0131n do\u011fum uzman\u0131n\u0131n bebe\u011fin kalbini yeterince g\u00f6r\u00fcnt\u00fcleyememesi veya kalp hastal\u0131\u011f\u0131ndan \u015f\u00fcphe etmesi<\/li><li>11-14 hafta ultrasonografik ense saydaml\u0131\u011f\u0131 testinde, artm\u0131\u015f ense kal\u0131nl\u0131\u011f\u0131 saptanmas\u0131 ( \u2265 3.5 mm): risk %6<\/li><li>Bebe\u011fin kalp h\u0131z\u0131nda h\u0131zlanma ve yava\u015flama saptanmas\u0131 (ta\u015fiaritmi veya blok)<\/li><li>Bebekte kalp d\u0131\u015f\u0131nda ba\u015fka bir do\u011fumsal anomali varl\u0131\u011f\u0131: mutlak risk %20-45<\/li><li><strong>Tek g\u00f6bek kordunu arteri varl\u0131\u011f\u0131<\/strong>: do\u011fumsal kalp hastal\u0131\u011f\u0131 ile birliktelik %4<\/li><li><strong>Monokoryonik ikiz<\/strong>: do\u011fumsal kalp hastal\u0131\u011f\u0131 birlikteli\u011fi %2-9, ikizden-ikize transf\u00fczyon sendromunda risk %10<\/li><li><strong>Hidrops Fetalis<\/strong>&nbsp;(\u2265 2 kompartmanda s\u0131v\u0131 birikimi) : do\u011fumsal kalp hastal\u0131\u011f\u0131 veya aritmi birlikteli\u011fi %15-25<\/li><\/ol>\n\n\n\n<div class=\"wp-block-image\"><figure class=\"aligncenter size-full\"><img fetchpriority=\"high\" decoding=\"async\" width=\"400\" height=\"266\" src=\"https:\/\/www.bursacocukkardiyoloji.com\/wp-content\/uploads\/2020\/03\/unnamed-2-2.jpg\" alt=\"\" class=\"wp-image-743\" srcset=\"https:\/\/www.bursacocukkardiyoloji.com\/wp-content\/uploads\/2020\/03\/unnamed-2-2.jpg 400w, https:\/\/www.bursacocukkardiyoloji.com\/wp-content\/uploads\/2020\/03\/unnamed-2-2-300x200.jpg 300w\" sizes=\"(max-width: 400px) 100vw, 400px\" \/><\/figure><\/div>\n\n\n\n<p><strong>Fetal ekokardiyografi&nbsp;<\/strong>ideal olarak&nbsp;<strong>16 \u2013 24. hamilelik haftas\u0131nda<\/strong>&nbsp;yap\u0131lmaktad\u0131r. Ancak \u015f\u00fcpheli bir bulgu saptanmas\u0131 durumunda 14. haftadan sonra gebeli\u011fin her d\u00f6neminde yap\u0131labilir. \u00c7al\u0131\u015fma 15-30 dakika kadar s\u00fcrmekle beraber, bebe\u011fin yerle\u015fimine, g\u00f6r\u00fcnt\u00fcn\u00fcn netli\u011fine ba\u011fl\u0131 olarak daha uzun s\u00fcrebilir. Bazen birden fazla da inceleme yapmak gerekebilir.<\/p>\n\n\n\n<p>Bu \u00e7al\u0131\u015fma s\u0131ras\u0131nda gebelik haftas\u0131, duru\u015fu, annenin a\u015f\u0131r\u0131 kilolu olmas\u0131, g\u00f6r\u00fcnt\u00fc kalitesinin yetersiz olmas\u0131 nedeni ile&nbsp;<strong>fetal ekokardiyografinin<\/strong>&nbsp;do\u011fumsal kalp hastal\u0131klar\u0131n\u0131 saptama oran\u0131 % 90 civar\u0131ndad\u0131r. Ya\u015fam\u0131 tehdit eden ciddi kalp anomalilerinde yan\u0131lma oran\u0131 \u00e7ok d\u00fc\u015f\u00fck olmakla birlikte, kapaklar ve b\u00fcy\u00fck damarlardaki hafif darl\u0131klar, k\u00fc\u00e7\u00fck atriyal veya ventrik\u00fcler septal defektler (k\u00fc\u00e7\u00fck delikler) g\u00f6zden ka\u00e7abilir. Bunun nedenleri aras\u0131nda baz\u0131 hastal\u0131klar\u0131n do\u011fumdan sonra hastal\u0131k haline gelmesi ve baz\u0131 deformitelerin ilerleyici olmas\u0131 da say\u0131labilir. Saptanan baz\u0131 anomalilerde de do\u011fuma kadar kaybolabilir.<\/p>\n\n\n\n<p>Fetal EKO ile bebe\u011fe oranla olduk\u00e7a k\u00fc\u00e7\u00fck bir kalp incelemektedir, dolay\u0131s\u0131yla g\u00f6r\u00fcnt\u00fcler genellikle bebek do\u011fduktan sonra oldu\u011fu kadar net de\u011fildir. Do\u011fumdan \u00f6nce g\u00f6r\u00fclen herhangi bir kalp kusurunun tan\u0131s\u0131, bebek do\u011fduktan sonra yap\u0131lacak bir ekokardiyografik inceleme ile do\u011frulanmal\u0131d\u0131r.<\/p>\n\n\n\n<p><strong>Bebe\u011finizde bir kalp anomalisi saptan\u0131rsa<\/strong>:<\/p>\n\n\n\n<p>Bebe\u011fin do\u011fumundan \u00f6nce tespit edilen herhangi bir \u00f6nemli anormallik, hamilelik boyunca pediatrik kardiyolog, kad\u0131n-do\u011fum ve perinatoloji uzman\u0131 taraf\u0131ndan takip edilecektir. Bu, bebe\u011fin kalbinin kalp yetmezli\u011fine girmemesini ve erken m\u00fcdahale gerektirmemesini sa\u011flamak i\u00e7indir. Amac\u0131m\u0131z, bebe\u011fin iyi olmad\u0131\u011f\u0131na dair kan\u0131t olmad\u0131k\u00e7a, m\u00fcmk\u00fcn oldu\u011funca do\u011fum tarihine yak\u0131n do\u011fum yapmaya \u00e7al\u0131\u015fmak ve erken do\u011fum yapmamakt\u0131r. Ya\u015fam\u0131n ilk haftas\u0131nda ameliyat olmas\u0131 bekleniyorsa, \u00f6nemli kalp anomalileri bir pediatrik kalp merkezinde do\u011fum gerektirebilir.<\/p>\n\n\n\n<p><strong>Prenatal tan\u0131 bize nas\u0131l yard\u0131mc\u0131 olur ?<\/strong><\/p>\n\n\n\n<p>Hipoplastik sa\u011f kalp, pulmoner atrezi veya kritik pulmoner stenoz gibi baz\u0131 sa\u011f kalp kusurlar\u0131 o kadar \u015fiddetlidir ki, bebeklerin mavi olmamas\u0131 i\u00e7in pulmoner arterlere kan ak\u0131\u015f\u0131 sa\u011flamak ve Hipoplastik sol kalp veya kritik koarktasyon gibi baz\u0131 sol kalp kusurlar\u0131, aorta perf\u00fcze etmek ve kan bas\u0131nc\u0131n\u0131 korumak i\u00e7in duktus arteriozusun (fetal yap\u0131) a\u00e7\u0131kl\u0131\u011f\u0131n\u0131n do\u011fum sonras\u0131 mutlak devam etmesi gerekir. Bu ve benzeri kalp kusurlar\u0131n\u0131n do\u011fum \u00f6ncesi tespit edilmesi, duktusun a\u00e7\u0131k kalmas\u0131n\u0131 sa\u011flayan bir ila\u00e7 olan prostaglandinlere do\u011fumdan sonra ba\u015flanmas\u0131 gerekti\u011fi konusunda doktorlar\u0131 uyar\u0131r. Duktusa ba\u011fl\u0131 kritik bir kalp kusuru do\u011fum \u00f6ncesi tespit edilemez ve duktus kapan\u0131rsa bebek hayatta kalmayabilir. Prenatal tan\u0131, \u00f6nemli ve muhtemelen ya\u015fam\u0131 tehdit eden kalp kusurlar\u0131 olan bebeklerin bir pediatrik kalp merkezinde do\u011fmas\u0131n\u0131 sa\u011flar. <meta charset=\"utf-8\">Bu durum, ailenin do\u011fum i\u00e7in haz\u0131rlanmas\u0131n\u0131, yenido\u011fan YB\u00dc&#8217; ni gezmesini, gerekirse kalp cerrahlar\u0131yla g\u00f6r\u00fc\u015fmesini, dolay\u0131s\u0131yla do\u011fumdan sonra ne olaca\u011f\u0131 konusunda daha rahat olmas\u0131n\u0131 sa\u011flar. Ayn\u0131 zamanda do\u011fum, yenido\u011fan bak\u0131m\u0131 ve kalp ameliyat\u0131n\u0131n ayn\u0131 hastanede yap\u0131lmas\u0131 sa\u011flanm\u0131\u015f olur.<\/p>\n\n\n\n<p> <\/p>\n","protected":false},"excerpt":{"rendered":"<p>Gebelikte bebe\u011fin kalp anomalileri a\u00e7\u0131s\u0131ndan de\u011ferlendirilmesini sa\u011flayan ultrasonografik bir g\u00f6r\u00fcnt\u00fcleme y\u00f6ntemi. Do\u011fumsal kalp hastal\u0131klar\u0131, s\u0131k g\u00f6r\u00fclmesine ra\u011fmen, rutin ultrasonografik inceleme esnas\u0131nda en s\u0131k g\u00f6zden ka\u00e7\u0131r\u0131lan anomalidir. Do\u011fumda en s\u0131k rastlan\u0131lan anomali olan Do\u011fumsal Kalp Hastal\u0131klar\u0131, canl\u0131 yenido\u011fanlar\u0131n 1\/100\u2019 inde g\u00f6r\u00fclmekte olup kromozom anormalisi varl\u0131\u011f\u0131nda s\u0131kl\u0131\u011f\u0131 6-7 kat daha artmaktad\u0131r. Do\u011fumsal kalp hastal\u0131klar\u0131, \u00f6nemli bir sa\u011fl\u0131k sorunu ve en s\u0131k rastlan\u0131lan [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":5677,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[11],"tags":[],"class_list":["post-5871","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-departments-medical"],"_links":{"self":[{"href":"https:\/\/www.bursacocukkardiyoloji.com\/index.php\/wp-json\/wp\/v2\/posts\/5871","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/www.bursacocukkardiyoloji.com\/index.php\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/www.bursacocukkardiyoloji.com\/index.php\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/www.bursacocukkardiyoloji.com\/index.php\/wp-json\/wp\/v2\/users\/1"}],"replies":[{"embeddable":true,"href":"https:\/\/www.bursacocukkardiyoloji.com\/index.php\/wp-json\/wp\/v2\/comments?post=5871"}],"version-history":[{"count":6,"href":"https:\/\/www.bursacocukkardiyoloji.com\/index.php\/wp-json\/wp\/v2\/posts\/5871\/revisions"}],"predecessor-version":[{"id":6386,"href":"https:\/\/www.bursacocukkardiyoloji.com\/index.php\/wp-json\/wp\/v2\/posts\/5871\/revisions\/6386"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/www.bursacocukkardiyoloji.com\/index.php\/wp-json\/wp\/v2\/media\/5677"}],"wp:attachment":[{"href":"https:\/\/www.bursacocukkardiyoloji.com\/index.php\/wp-json\/wp\/v2\/media?parent=5871"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/www.bursacocukkardiyoloji.com\/index.php\/wp-json\/wp\/v2\/categories?post=5871"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/www.bursacocukkardiyoloji.com\/index.php\/wp-json\/wp\/v2\/tags?post=5871"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}